NameNADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial
Synonyms
  • CI-9kD
  • Complex I-9kD
  • NADH-ubiquinone oxidoreductase 9 kDa subunit
  • Renal carcinoma antigen NY-REN-4
Gene NameNDUFV3
OrganismHuman
Amino acid sequence
>lcl|BSEQ0000054|NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial
MAAPCLLRQGRAGALKTMLQEAQVFRGLASTVSLSAESGKSEKGQPQNSKKQSPPKKPAP
VPAEPFDNTTYKNLQHHDYSTYTFLDLNLELSKFRMPQPSSGRESPRH
Number of residues108
Molecular Weight11940.435
Theoretical pI10.3
GO Classification
Functions
  • NADH dehydrogenase (ubiquinone) activity
  • poly(A) RNA binding
Processes
  • mitochondrial electron transport, NADH to ubiquinone
  • small molecule metabolic process
  • cellular metabolic process
  • respiratory electron transport chain
Components
  • mitochondrion
  • mitochondrial inner membrane
  • nucleoplasm
  • mitochondrial respiratory chain complex I
General FunctionPoly(a) rna binding
Specific FunctionAccessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone.
Pfam Domain Function
Transmembrane RegionsNot Available
GenBank Protein ID6002197
UniProtKB IDP56181
UniProtKB Entry NameNDUV3_HUMAN
Cellular LocationMitochondrion inner membrane
Gene sequence
>lcl|BSEQ0016002|NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial (NDUFV3)
ATGGCTGCCCCGTGTTTGCTGCGGCAAGGACGAGCCGGGGCGCTGAAGACTATGCTCCAG
GAAGCCCAGGTGTTTCGAGGACTTGCTTCTACGGTTTCTTTGTCTGCGGAATCAGGGAAG
AGTGAAAAGGGTCAGCCACAGAATTCCAAGAAGCAAAGTCCACCAAAAAAGCCAGCCCCA
GTGCCTGCTGAGCCGTTTGACAACACTACCTACAAGAACCTGCAGCATCATGACTACAGC
ACGTACACCTTCTTAGACCTCAACCTCGAACTCTCAAAATTCAGGATGCCTCAGCCCTCC
TCAGGCCGGGAGTCACCTCGACACTGA
GenBank Gene IDX99726
GeneCard IDNot Available
GenAtlas IDNDUFV3
HGNC IDHGNC:7719
Chromosome Location21
LocusNot Available
References
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